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十七、表皮样囊肿
桥小脑角占一半,形态多呈不规状。
弥散受限信号高,见缝就钻是特点。
口诀解读:
表皮样囊肿是由神经管闭合期间外胚层细胞移行异常所致,病理上病变囊壁菲薄,由一层表皮组织形成,囊内由上皮碎屑、角蛋白和胆固醇组成。好发于青壮年,约一半发生在桥小脑角区。影像学上病变呈不规则状囊性肿块,通常沿蛛网膜下腔匍匐生长,有见缝就钻特点,CT上90%呈低密度,MRI信号较复杂,T 1WI多呈略高于脑脊液信号,T 2WI呈高信号,DWI明显受限也呈高信号,增强扫描未见强化(图1-22)。
![](https://epubservercos.yuewen.com/E8BE36/19400084508708206/epubprivate/OEBPS/Images/P36_36_1_1147.jpg?sign=1738879766-vu3c7woVLWlvs9UsRsuVQ1AMwMmIJU4M-0-4cd6fe48a2becb0226025a8f2d03caa0)
![](https://epubservercos.yuewen.com/E8BE36/19400084508708206/epubprivate/OEBPS/Images/P36_36_2_1148.jpg?sign=1738879766-9eFUOos2lfDXCaZZkqYfzEaxJ92UI72A-0-c5449bb4fa2707b1451b4ca22a4b1b5c)
![](https://epubservercos.yuewen.com/E8BE36/19400084508708206/epubprivate/OEBPS/Images/P1-22_1151.jpg?sign=1738879766-5FHNscTy2BIbtUqelhBfy0qiKnUP9mxL-0-d27a648cbe15aea31a1db5607ba907cd)
图1-22 表皮样囊肿
A.MRI横轴位T 1WI;B.T 2WI横轴位;C.DWI
![](https://epubservercos.yuewen.com/E8BE36/19400084508708206/epubprivate/OEBPS/Images/P1-22_1175.jpg?sign=1738879766-Rk0tm8BsNmrccXFgbNiZdXse2tM8UHJE-0-f429da24cd921cbeaab28740628c0fcc)
图1-22 表皮样囊肿(续)
D.对比增强,示右侧桥小脑角区不规则异常信号肿块,沿邻近蛛网膜下腔向桥前池生长,T 1WI信号略高于脑脊液,T 2WI呈高信号,DWI仍呈高信号,增强扫描无强化